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KMID : 1103720120660030263
Journal of the Korean Society of Radiology
2012 Volume.66 No. 3 p.263 ~ p.266
Serial CT Findings of Resolving Extramedullary Hematopoiesis as Unilateral Posterior Mediastinal Mass after Splenectomy in Hereditary Spherocytosis: A Case Report
Nam Mi-Yeon

Lee Ju-Won
Kim Yeo-Ju
Kim Youn-Jeong
Kang Young-Hye
Lee Kyung-Hee
Abstract
Intrathoracic extramedullary hematopoiesis (EMH) is a rare condition of the hereditary spherocytosis. EMH usually regresses or disappears after treatment; such as splenectomy in the case of spherocytosis. We report a case of hereditary spherocytosis. It is presented with an unilateral paravertebral posterior mediastinal mass. After splenectomy, it revealed shrinkage and fatty replacement on serial CT scans.
KEYWORD
Extramedullary Hematopoiesis, Posterior Mediastinal Mass, Hereditary Spherocytosis
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